dc.contributor | Vall d'Hebron Barcelona Hospital Campus |
dc.contributor.author | Real Martinez, Alberto |
dc.contributor.author | Brull, Astrid |
dc.contributor.author | Huerta Alonso, Jordi |
dc.contributor.author | Tarrasó Urios, Guillermo |
dc.contributor.author | Lucia, Alejandro |
dc.contributor.author | Martín, Miguel A. |
dc.contributor.author | Andreu Périz, Antonio Luis |
dc.contributor.author | Pinós Figueras, Tomàs |
dc.date.accessioned | 2019-05-23T10:37:05Z |
dc.date.available | 2019-05-23T10:37:05Z |
dc.date.issued | 2019-03-26 |
dc.identifier.citation | Real-Martinez A, Brull A, Huerta J, Tarrasó G, Lucia A, Martin MA, et al. Low survival rate and muscle fiber-dependent aging effects in the McArdle disease mouse model. Sci Rep. 2019;9(1):5116. |
dc.identifier.issn | 2045-2322 |
dc.identifier.uri | https://hdl.handle.net/11351/4083 |
dc.description | Taxa de supervivència; Malaltia de McArdle; Model de ratolí |
dc.description.sponsorship | ISCIII CD14/00032/Ministry of Economy and Competitiveness | Instituto de Salud Carlos III (Institute of Health Carlos III) |
dc.language.iso | eng |
dc.publisher | Nature Research |
dc.relation.ispartofseries | Scientific Reports;9(1) |
dc.rights | Attribution-NonCommercial-NoDerivatives 4.0 International |
dc.rights.uri | http://creativecommons.org/licenses/by-nc-nd/4.0/ |
dc.source | Scientia |
dc.subject | Glicogenosi - Mortalitat |
dc.subject | Ratolins - Metabolisme |
dc.subject.mesh | Glycogen Storage Disease Type V |
dc.subject.mesh | /mortality |
dc.subject.mesh | /metabolism |
dc.subject.mesh | Mice |
dc.subject.mesh | Models, Animal |
dc.title | Low survival rate and muscle fiber-dependent aging effects in the McArdle disease mouse model |
dc.type | info:eu-repo/semantics/article |
dc.identifier.doi | 10.1038/s41598-019-41414-8 |
dc.subject.decs | enfermedad por almacenamiento de glucógeno tipo V |
dc.subject.decs | /mortalidad |
dc.subject.decs | /metabolismo |
dc.subject.decs | ratones |
dc.subject.decs | modelos animales |
dc.relation.publishversion | https://www.nature.com/articles/s41598-019-41414-8 |
dc.type.version | info:eu-repo/semantics/publishedVersion |
dc.audience | Professionals |
dc.contributor.organismes | Institut Català de la Salut |
dc.contributor.authoraffiliation | [Real-Martinez A, Huerta J, Tarrasó G] Grup de recerca en Patologia Neuromuscular i Mitocondrial, Vall d’Hebron Institut de Recerca, Barcelona, Spain. Universitat Autònoma de Barcelona, Barcelona, Spain. [Brull A] Sorbonne Université, Center of Research in Myology, Paris, France. [Lucia A] Faculty of Sport Sciences, Universidad Europea de Madrid, Madrid, Spain. Mitochondrial and Neuromuscular Diseases Laboratory, 12 de Octubre Hospital Research Institute (i+ 12), Madrid, Spain. Centro de Investigación Biomédica en Red de Enfermedades Raras (CIBERER), Madrid, Spain. [Martin MA] Mitochondrial and Neuromuscular Diseases Laboratory, 12 de Octubre Hospital Research Institute (i+ 12), Madrid, Spain. Centro de Investigación Biomédica en Red de Enfermedades Raras (CIBERER), Madrid, Spain. [Andreu AL, Pinós T] Grup de recerca en Patologia Neuromuscular i Mitocondrial, Vall d’Hebron Institut de Recerca, Barcelona, Spain. Universitat Autònoma de Barcelona, Barcelona, Spain. Centro de Investigación Biomédica en Red de Enfermedades Raras (CIBERER), Madrid, Spain. |
dc.identifier.pmid | 30914683 |
dc.identifier.wos | WOS:000462298600003 |
dc.rights.accessrights | info:eu-repo/semantics/openAccess |