dc.contributor | Vall d'Hebron Barcelona Hospital Campus |
dc.contributor.author | Sansa, Alba |
dc.contributor.author | Hidalgo, Ivan |
dc.contributor.author | Miralles, Maria P. |
dc.contributor.author | de la Fuente, Sandra |
dc.contributor.author | Pérez García, Maria Jose |
dc.contributor.author | Munell Casadesus, Francina |
dc.date.accessioned | 2022-04-07T12:17:15Z |
dc.date.available | 2022-04-07T12:17:15Z |
dc.date.issued | 2021-07-03 |
dc.identifier.citation | Sansa A, Hidalgo I, Miralles MP, de la Fuente S, Perez-Garcia MJ, Munell F, et al. Spinal Muscular Atrophy autophagy profile is tissue-dependent: differential regulation between muscle and motoneurons. Acta Neuropathol Commun. 2021 Jul 3;9:122. |
dc.identifier.issn | 2051-5960 |
dc.identifier.uri | https://hdl.handle.net/11351/7328 |
dc.description | Motoneurona; Neurodegeneració; Malaltia neuromuscular |
dc.description.sponsorship | The authors wish to thank the consenting parents and patients. This work was supported by grants from Instituto de Salud Carlos III, Fondo de Inversiones Sanitarias, Unión Europea, Fondo Europeo de Desarrollo Regional (FEDER) “Una manera de hacer Europa” (PI17/00231, PI20/00098), AGAUR (2014 SGR 1087), and Fundació La Marató TV3 (73/C/2020). AG is a Serra Hunter Fellow from Generalitat de Catalunya, AS holds a fellowship from Universitat de Lleida and M.J.P-G was awarded the Marie-Curie fellowship (BP-B 00083). We thank Elaine Lilly, PhD, for English language revision of the manuscript. |
dc.language.iso | eng |
dc.publisher | BMC |
dc.relation.ispartofseries | Acta Neuropathologica Communications;9 |
dc.rights | Attribution 4.0 International |
dc.rights.uri | http://creativecommons.org/licenses/by/4.0/ |
dc.source | Scientia |
dc.subject | Atròfia muscular espinal - Patogènesi |
dc.subject | Autofàgia - Patogènesi |
dc.subject | Múscul estriat - Patogènesi |
dc.subject.mesh | Muscular Atrophy, Spinal |
dc.subject.mesh | Muscle, Skeletal |
dc.subject.mesh | Autophagy |
dc.title | Spinal Muscular Atrophy autophagy profile is tissue-dependent: differential regulation between muscle and motoneurons |
dc.type | info:eu-repo/semantics/article |
dc.identifier.doi | 10.1186/s40478-021-01223-5 |
dc.subject.decs | atrofia muscular espinal |
dc.subject.decs | músculo esquelético |
dc.subject.decs | autofagia |
dc.relation.publishversion | https://doi.org/10.1186/s40478-021-01223-5 |
dc.type.version | info:eu-repo/semantics/publishedVersion |
dc.audience | Professionals |
dc.contributor.organismes | Institut Català de la Salut |
dc.contributor.authoraffiliation | [Sansa A, Hidalgo I, Miralles MP, de la Fuente S] Neuronal Signaling Unit, Experimental Medicine Department, Universitat de Lleida-IRBLleida, 25198 Lleida, Spain. [Perez-Garcia MJ, Munell F] Grup de Recerca en Neurologia Pediàtrica, Vall d’Hebron Institut de Recerca (VHIR), Barcelona, Spain. Unitat de Trastorns Neuromusculars Pediàtrics, Vall d’Hebron Hospital Universitari, Barcelona, Spain |
dc.identifier.pmid | 34217376 |
dc.identifier.wos | 000669285200001 |
dc.rights.accessrights | info:eu-repo/semantics/openAccess |