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dc.contributorVall d'Hebron Barcelona Hospital Campus
dc.contributor.authorSansa, Alba
dc.contributor.authorHidalgo, Ivan
dc.contributor.authorMiralles, Maria P.
dc.contributor.authorde la Fuente, Sandra
dc.contributor.authorPérez García, Maria Jose
dc.contributor.authorMunell Casadesus, Francina
dc.date.accessioned2022-04-07T12:17:15Z
dc.date.available2022-04-07T12:17:15Z
dc.date.issued2021-07-03
dc.identifier.citationSansa A, Hidalgo I, Miralles MP, de la Fuente S, Perez-Garcia MJ, Munell F, et al. Spinal Muscular Atrophy autophagy profile is tissue-dependent: differential regulation between muscle and motoneurons. Acta Neuropathol Commun. 2021 Jul 3;9:122.
dc.identifier.issn2051-5960
dc.identifier.urihttps://hdl.handle.net/11351/7328
dc.descriptionMotoneurona; Neurodegeneració; Malaltia neuromuscular
dc.description.sponsorshipThe authors wish to thank the consenting parents and patients. This work was supported by grants from Instituto de Salud Carlos III, Fondo de Inversiones Sanitarias, Unión Europea, Fondo Europeo de Desarrollo Regional (FEDER) “Una manera de hacer Europa” (PI17/00231, PI20/00098), AGAUR (2014 SGR 1087), and Fundació La Marató TV3 (73/C/2020). AG is a Serra Hunter Fellow from Generalitat de Catalunya, AS holds a fellowship from Universitat de Lleida and M.J.P-G was awarded the Marie-Curie fellowship (BP-B 00083). We thank Elaine Lilly, PhD, for English language revision of the manuscript.
dc.language.isoeng
dc.publisherBMC
dc.relation.ispartofseriesActa Neuropathologica Communications;9
dc.rightsAttribution 4.0 International
dc.rights.urihttp://creativecommons.org/licenses/by/4.0/
dc.sourceScientia
dc.subjectAtròfia muscular espinal - Patogènesi
dc.subjectAutofàgia - Patogènesi
dc.subjectMúscul estriat - Patogènesi
dc.subject.meshMuscular Atrophy, Spinal
dc.subject.meshMuscle, Skeletal
dc.subject.meshAutophagy
dc.titleSpinal Muscular Atrophy autophagy profile is tissue-dependent: differential regulation between muscle and motoneurons
dc.typeinfo:eu-repo/semantics/article
dc.identifier.doi10.1186/s40478-021-01223-5
dc.subject.decsatrofia muscular espinal
dc.subject.decsmúsculo esquelético
dc.subject.decsautofagia
dc.relation.publishversionhttps://doi.org/10.1186/s40478-021-01223-5
dc.type.versioninfo:eu-repo/semantics/publishedVersion
dc.audienceProfessionals
dc.contributor.organismesInstitut Català de la Salut
dc.contributor.authoraffiliation[Sansa A, Hidalgo I, Miralles MP, de la Fuente S] Neuronal Signaling Unit, Experimental Medicine Department, Universitat de Lleida-IRBLleida, 25198 Lleida, Spain. [Perez-Garcia MJ, Munell F] Grup de Recerca en Neurologia Pediàtrica, Vall d’Hebron Institut de Recerca (VHIR), Barcelona, Spain. Unitat de Trastorns Neuromusculars Pediàtrics, Vall d’Hebron Hospital Universitari, Barcelona, Spain
dc.identifier.pmid34217376
dc.identifier.wos000669285200001
dc.rights.accessrightsinfo:eu-repo/semantics/openAccess


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